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Transcatheter management of mid-aortic syndrome secondary to myofibroma presenting in infancy with severe left ventricular dysfunction: a case report

Published online by Cambridge University Press:  08 October 2015

Ryan Callahan ,
Jacqueline Kreutzer  and
Mark Debrunner
Ryan Callahan*
Affiliation:
Department of Cardiology, Boston Children’s Hospital and Harvard Medical School, Boston, Massachusetts, United States of America
Jacqueline Kreutzer
Affiliation:
University of Pittsburgh Medical School, University of Pittsburgh Medical Center, Division of Cardiology, Children’s Hospital of Pittsburgh, Pittsburgh, Pennsylvania, United States of America
Mark Debrunner
Affiliation:
University of Pittsburgh Medical School, University of Pittsburgh Medical Center, Division of Cardiology, Children’s Hospital of Pittsburgh, Pittsburgh, Pennsylvania, United States of America
*
Correspondence to: R. Callahan, MD, Department of Cardiology, Boston Children’s Hospital, 300 Longwood Ave, Boston, MA 02115, United States of America. Tel: +617 355 6529; Fax: +617 730 7548; E-mail: ryan.callahan@cardio.chboston.org
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Abstract

In this study, we summarise a case of a myofibroma causing mid-aortic syndrome due to obstruction of the distal thoracic and abdominal aorta leading to severe left ventricular dysfunction. The patient was managed with percutaneous intervention via balloon dilation and stent placement. On follow-up, the patient has normalisation of ventricular function, is off anti-hypertensives, and is being monitored for re-stenosis.

Keywords

Catheterisationmid-aortic syndromemyofibroma
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Issue 4 , April 2016 , pp. 799 - 801
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Copyright
© Cambridge University Press 2015 

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