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Three-dimensional echocardiographic evaluation of Ebstein’s anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome

Part of: Echocardiography Hypoplastic Left Heart Syndrome (HLHS)

Published online by Cambridge University Press:  22 April 2018

Courtney Cassidy Open the ORCID record for Courtney Cassidy [Opens in a new window] ,
Max B. Mitchell  and
Pei-Ni Jone
Courtney Cassidy*
Affiliation:
Children’s Hospital Colorado, Aurora, CO, USA
Max B. Mitchell
Affiliation:
Cardiovascular Surgery, Children’s Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA
Pei-Ni Jone
Affiliation:
Pediatric Cardiology, Children’s Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA
*
Author for correspondence: C. Cassidy, RDCS, Children’s Hospital Colorado, 13123 East 16th Avenue, Aurora, CO 80045, USA. Tel: 720 777 2949; Fax: 1 720 777 7174; E-mail: courtney.cassidy@childrenscolorado.org
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Abstract

We report three-dimensional imaging of a rare finding of Ebstein’s anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome, which has been previously reported only by two-dimensional echocardiography. A fetal echocardiogram was performed at 19 weeks that showed a moderately hypoplastic left ventricle, severely hypoplastic mitral valve, a severely hypoplastic aortic valve, and a dysplastic tricuspid valve. Post Caesarean delivery at 40 weeks of gestation, a transthoracic echocardiogram confirmed the findings seen on the fetal echocardiogram. A three-dimensional echocardiogram was then performed, which demonstrated an Ebstein tricuspid valve with apical displacement of the septal leaflet, chordal attachments of the valve to the right ventricular outflow tract, and moderate tricuspid regurgitation. The patient underwent a successful heart transplantation.

Keywords

Ebstein’s anomalyhypoplastic left heart syndrome3D echocardiographytricuspid valve regurgitationechocardiography and scans
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 6 , June 2018 , pp. 885 - 887
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Copyright
© Cambridge University Press 2018 

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References

1. Gobergs, R, Salputra, E, Lubaua, I. Hypoplastic left heart syndrome: a review. Acta Med Litu 2016; 23: 86–98.Google ScholarPubMed
2. Luxford, JC, Arora, N, Ayer, JG, et al. Neonatal Ebstein anomaly: a 30-year institutional review. Semin Thorac Cardiovasc Surg 2017; 29: 206–212.Google Scholar
3. Stamm, C, Anderson, RH, Ho, SY. The morphologically tricuspid valve in hypoplastic left heart syndrome. Eur J Cardiothorac Surg 1997; 12: 587–592.Google Scholar
4. Werho, DK, Thorsson, T, Owens, ST, Fifer, C. Biventricular badness: rare images of Ebstein anomaly of the tricuspid valve in a patient with hypoplastic left heart syndrome. Pediatr Cardiol 2015; 36: 1310–1311.CrossRefGoogle Scholar
5. Hammel, JM, Danford, DA, Spicer, RL, Kutty, S. Fetal and neonatal imaging and strategy of primary neonatal heart transplantation in hypoplastic left heart with Ebstein’s anomaly. Echocardiography 2015; 32: 598–601.CrossRefGoogle ScholarPubMed
6. Castaneda-Zuniga, W, Nath, HP, Moller, JH, Edwards, JE. Left-sided anomalies in Ebstein’s malformation of the tricuspid valve. Pediatr Cardiol 1982; 3: 181–185.CrossRefGoogle ScholarPubMed
7. Kutty, S, Graney, BA, Khoo, NS, et al. Serial assessment of right ventricular volume and function in surgically palliated hypoplastic left heart syndrome using real-time transthoracic three-dimensional echocardiography. J Am Soc Echocardiogr 2012; 25: 682–689.CrossRefGoogle ScholarPubMed
8. Bharucha, T, Anderson, RH, Lim, ZS, Vettukattil, JJ. Multiplanar review of three-dimensional echocardiography gives new insights into the morphology of Ebstein’s malformation. Cardiol Young 2010; 20: 49–53.CrossRefGoogle ScholarPubMed
9. Acar, P, Abadir, S, Roux, D, et al. Ebstein’s anomaly assessed by real-time 3-D echocardiography. Ann Thorac Surg 2006; 82: 731–733.Google Scholar
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