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Repair in infancy of tetralogy of Fallot with absence of the leaflets of the pulmonary valve (absent pulmonary valve syndrome) using a valved pulmonary artery homograft

Published online by Cambridge University Press:  19 August 2008

Delores Danilowicz ,
Salvatore Presti ,
Stephen B. Colvin  and
Eugenie F. Doyle
Delores Danilowicz*
Affiliation:
Departments of Pediatrics and Cardiovascular Surgery, New York University Medical Center, New York
Salvatore Presti
Affiliation:
Departments of Pediatrics and Cardiovascular Surgery, New York University Medical Center, New York
Stephen B. Colvin
Affiliation:
Departments of Pediatrics and Cardiovascular Surgery, New York University Medical Center, New York
Eugenie F. Doyle
Affiliation:
Departments of Pediatrics and Cardiovascular Surgery, New York University Medical Center, New York
*
Dr. Delores Damlowicz, Tisch University Hospital, Room 576, 560 First Avenue, New York, NY 10016, USA
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Summary

Two infants, aged eight days and four months, with tetralogy of Fallot and absence of the leaflets of the pulmonary valve, presented with acute respiratory distress and congestive heart failure. Primary repair was performed using a cryopreserved pulmonary arterial homograft. Both infants survived and are doing well three and two years later. A review of the surgical procedures attempted in this symptomatic group of patients is presented together with a discussion of the pathophysiology of this defect.

Keywords

Tetralogy of Fallotabsent pulmonary valvepulmonary arterial homograft
Type
Original Articles
Information
Cardiology in the Young , Volume 2 , Issue 1 , January 1992 , pp. 25 - 29
Copyright
Copyright © Cambridge University Press 1992

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