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Rare combination of bilateral divided atrial chambers and pulmonary vein stenosis with review of the literature

Published online by Cambridge University Press:  16 June 2014

Faris Al-Mousily ,
Ghassan Baslaim ,
Amjad Kouatli ,
Jameel Al-Ata  and
Amin M. Arfi
Faris Al-Mousily
Affiliation:
Department of Cardiovascular Diseases, King Faisal Specialist Hospital & Research Center Gen. Org. Jeddah, Kingdom of Saudi Arabia Department of Pediatrics, University of Florida, Gainesville, United States of America
Ghassan Baslaim
Affiliation:
Department of Cardiovascular Diseases, King Faisal Specialist Hospital & Research Center Gen. Org. Jeddah, Kingdom of Saudi Arabia
Amjad Kouatli
Affiliation:
Department of Cardiovascular Diseases, King Faisal Specialist Hospital & Research Center Gen. Org. Jeddah, Kingdom of Saudi Arabia
Jameel Al-Ata
Affiliation:
Department of Cardiovascular Diseases, King Faisal Specialist Hospital & Research Center Gen. Org. Jeddah, Kingdom of Saudi Arabia
Amin M. Arfi*
Affiliation:
Department of Cardiovascular Diseases, King Faisal Specialist Hospital & Research Center Gen. Org. Jeddah, Kingdom of Saudi Arabia
*
Correspondence to: Dr A. M. Arfi, MBC J-16, PB 40047, Jeddah-21499, Kingdom of Saudi Arabia. Tel: +966 12 667 7777, ext. 62511; Fax: +966 12 667 7777, ext. 62162; E-mail: ped_cardiologist@doctor.com
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Abstract

Introduction: The term cor triatriatum is used to describe a fibromuscular partition that divides an atrium into two compartments. It was first used by Borst in 1905, although the lesion had been described before by Church in 1868. Both described divided left atrial chamber (also referred to as cor triatriatum sinister). The incidence of the divided left atrial chamber among patients with congenital heart disease is reported at 0.1% and 0.4% in an autopsy study. Divided right atrial chamber – also referred to as cor triatriatum dexter – is even rarer to an extent that there is no reported incidence and only few hundred cases have been reported so far. A search through pubMed library revealed only 90 publications on humans, either under the term “dexter” or “dextrum”. We would like to report a new association of bilateral divided atrial chambers and pulmonary vein stenosis, with a review of the literature.

Keywords

Cor triatriatumcongenital heart diseasepulmonary vein stenosis
Type
Review Articles
Information
Cardiology in the Young , Volume 25 , Supplement 2 , February 2015 , pp. 218 - 221
Copyright
© Cambridge University Press 2014 

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