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A puzzling CHD: a late diagnosis of left atrial isomerism

Published online by Cambridge University Press:  08 July 2022

Miguel Martins de Carvalho Open the ORCID record for Miguel Martins de Carvalho [Opens in a new window] ,
Mariana Vasconcelos ,
André Carvalho ,
Cristina Cruz  and
Filipe Macedo
Miguel Martins de Carvalho*
Affiliation:
Department of Cardiology, São João Universitary Hospital, Oporto, Portugal Cardiovascular R&D Center, Universidade do Porto Faculdade de Medicina, Portugal
Mariana Vasconcelos
Affiliation:
Department of Cardiology, São João Universitary Hospital, Oporto, Portugal
André Carvalho
Affiliation:
Department of Radiology, São João Universitary Hospital, Oporto, Portugal
Cristina Cruz
Affiliation:
Department of Cardiology, São João Universitary Hospital, Oporto, Portugal
Filipe Macedo
Affiliation:
Department of Cardiology, São João Universitary Hospital, Oporto, Portugal Cardiovascular R&D Center, Universidade do Porto Faculdade de Medicina, Portugal
*
Author for correspondence: Miguel Martins de Carvalho, Department of Cardiology, Alameda Prof. Hernani Monteiro, 4200-319 Porto, Portugal. Tel: +351967096459. E-mail: u014072@chsj.min-saude.pt
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Abstract

We present a case of a 41-year-old patient with an unknown complex cardiac anatomy, who was previously submitted to two cardiac surgeries. Using multimodality imaging, a retrospective diagnosis was established, revealing a heterotaxy syndrome (left isomerism).

Keywords

Adult CHDheterotaxy syndromemultimodality imagingheart failure
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 3 , March 2023 , pp. 479 - 481
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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