Skip to main content Accessibility help

A pulmonary artery sling with a vascular ring in a toddler: an uncommon combination

  • Ziyad M. Binsalamah (a1), Charles D. Fraser (a1) and Carlos M. Mery (a1)


Pulmonary artery slings and vascular rings are very rare congenital anomalies. It is even rarer to have both anomalies in the same setting. We present a case of a toddler who was diagnosed with a left pulmonary artery sling and a vascular ring as part of the screening process for the VACTERL association – co-occurrence of vertebral, anorectal, cardiac, tracheoesophageal, renal, and limb malformations. He underwent a successful surgical repair via median sternotomy and on cardiopulmonary bypass with an uneventful postoperative course.


Corresponding author

Author for correspondence: Z. M. Binsalamah, MD, MSc, FRCSC, Division of Congenital Heart Surgery, Texas Children’s Hospital; Michael E. DeBakey Department of Surgery, Baylor College of Medicine, 6621 Fannin St, MC19345H, Houston, TX 77030, USA. Tel: 832 826 1929; Fax: 832 825 1905; E-mail:


Hide All
1. Lee, JW, Printz, BF, Hegde, SR, Vargas, LA, Sun, HY. Double trouble: fetal diagnosis of a pulmonary artery sling and vascular ring. Clin Case Rep 2016; 4: 11871190.
2. Fiore, AC, Brown, JW, Weber, TR, Turrentine, MW. Surgical treatment of pulmonary artery sling and tracheal stenosis. Ann Thorac Surg 2005; 79: 3846; discussion 38–46.
3. Backer, CL, Russell, HM, Kaushal, S, Rastatter, JC, Rigsby, CK, Holinger, LD. Pulmonary artery sling: current results with cardiopulmonary bypass. J Thorac Cardiovasc Surg 2012; 143: 144151.
4. Potts, WJ, Holinger, PH, Rosenblum, AH. Anomalous left pulmonary artery causing obstruction to right main bronchus: report of a case. JAMA 1954; 155: 14091411.
5. Wu, SJ, Downing, T, Mascio, C, et al. Reintervention burden and vessel growth after surgical reimplantation of a pulmonary artery during childhood. Pediatr Cardiol 2018; 39: 390397.
6. Jeong, DH, Han, HS, Hahn, YS, Lee, SJ. Unusual association of pulmonary artery sling with right aortic arch and aberrant left subclavian artery. J Korean Med Sci 2000; 15: 119121.



Full text views

Total number of HTML views: 0
Total number of PDF views: 0 *
Loading metrics...

Abstract views

Total abstract views: 0 *
Loading metrics...

* Views captured on Cambridge Core between <date>. This data will be updated every 24 hours.

Usage data cannot currently be displayed