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Protein-losing enteropathy in biventricular circulation precipitated by mild stenosis of the inferior caval vein in conjunction with total occlusion of the superior caval vein: a word of caution

Published online by Cambridge University Press:  06 April 2017

Davide Marini ,
Brian A. McCrossan  and
Gabriella Agnoletti
Davide Marini*
Affiliation:
Department of Paediatric Cardiology, Ospedale Infantile Regina Margherita, Città della Salute e della Scienza, Turin, Italy Department of Public Health and Paediatrics, University of Turin, Turin, Italy
Brian A. McCrossan
Affiliation:
Department of Paediatric Cardiology, Royal Belfast Hospital for Sick Children, Belfast, Northern Ireland, UK
Gabriella Agnoletti
Affiliation:
Department of Paediatric Cardiology, Ospedale Infantile Regina Margherita, Città della Salute e della Scienza, Turin, Italy
*
Correspondence to: D. Marini, Department of Paediatric Cardiology, Ospedale Infantile Regina Margherita, Corso Spezia 60, 10126, Torino, Italy. Tel: +39 011 313 5492; Fax: +39 011 313 5482; E-mail: dmarini@cittadellasalute.to.it
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Abstract

We report the case of a young boy with a history of total occlusion of the superior caval vein, diagnosed early after complex neonatal cardiac surgery, who developed severe protein-losing enteropathy. Protein-losing enteropathy was precipitated by a relatively mild stenosis at the junction of the inferior caval vein with the right atrium. Percutaneous stent dilation of the veno-atrial junction definitively relieved the stenosis, and the protein-losing enteropathy subsequently resolved.

Keywords

Protein-losing enteropathysystemic vein occlusionCT
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 7 , September 2017 , pp. 1430 - 1433
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Copyright
© Cambridge University Press 2017 

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References

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