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New-onset cardiac rhabdomyoma beyond infancy in a patient with tuberous sclerosis complex

Published online by Cambridge University Press:  14 July 2015

Nikhil M. Thatte*
Affiliation:
Department of Pediatrics, University of Texas Southwestern Medical Center, Dallas, Texas, United States of America
Kristine J. Guleserian
Affiliation:
Division of Pediatric Cardiothoracic Surgery, University of Texas Southwestern Medical Center, Dallas, Texas, United States of America
Surendranath R. Veeram Reddy
Affiliation:
Division of Cardiology, Department of Pediatrics, University of Texas Southwestern Medical Center, Dallas, Texas, United States of America
*
Correspondence to: N. Thatte, MD, University of Texas Southwestern Medical Center/Children’s Medical Center, 1935 Medical District Drive, Dallas, Texas 75235, United States of America. Tel: +1-214-456-5518; Fax: +1-214-456-2625; E-mail: Nikhil.Thatte@Childrens.com

Abstract

Cardiac rhabdomyomas in patients with tuberous sclerosis complex are usually detected antenatally or during infancy, with subsequent stabilisation or spontaneous regression. Development of a new cardiac rhabdomyoma beyond infancy is very rare. We report a male child who needed resection of a large rhabdomyoma in neonatal life, and then developed a new-onset rhabdomyoma at 2 years of age in a different location, needing another resection. Routine surveillance for cardiac rhabdomyomas in asymptomatic patients with tuberous sclerosis is essential.

Type
Brief Reports
Copyright
© Cambridge University Press 2015 

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