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Myocarditis, flail tricuspid valve, and normal rhythm: an exceptional form of neonatal cardiac lupus

  • María-Teresa González-López (a1) (a2), Ramón Pérez-Caballero-Martínez (a1) (a2) and Juan-Miguel Gil-Jaurena (a1) (a2)


Neonatal cardiac lupus is a rare, passively acquired autoimmune disease. We report a case of in utero myocarditis, confirmed postnatally, with papillary muscle rupture and severe tricuspid regurgitation after birth in the absence of conduction disturbances. Tricuspid repair was successfully performed with polytetrafluoroethylene neochordae. In this article, we discuss the pathophysiology, medical and surgical management, and implications at follow-up in this unique scenario.


Corresponding author

Correspondence to: M.-T. González-López, MD, PhD, Pediatric Cardiac Surgery Department, Gregorio Marañón Hospital, C/ O’Donnell 48-50, 28009 Madrid, Spain. Tel: +34 616 23 19 44; Fax: +34 915 86 80 18; E-mail:


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