Skip to main content Accessibility help

Left-sided hepatic vein connected to the coronary sinus

  • László Király (a1), John E. Deanfield (a1) and Marc R. de Leval (a1)


A left-sided hepatic vein connected to the coronary sinus is reported in a case of a 22-month-old boy with isomerism of the left atrial appendages, complete atrioventricular septal defect and azygous continuation of the inferior caval vein. The diagnosis of the anomalous hepatic vein was made intraoperatively and successful biventricular repair has been accomplished. To the best of our knowledge, this is the first communication on this peculiar entity diagnosed during life, notwithstanding Nabarro's description of a similar autopsy finding in 1903. Aspects of the development of this rare entity are discussed.


Corresponding author

Mr. Marc de Leval, Cardiothoracic Unit, Great Ormond Street Hospital for Children, Great Ormond Street, London WC1N 3JH, United Kingdom. Tel. 44-171-404-4383; Fax. 44-171-831-4931.


Hide All
1.Anderson, RH, Sapire, DW. Atrial isomerism. In Anderson, RH, Shinebourne, EA, Macartney, FJ, Tynan, M. (eds). Paediatric Cardiology. Churchill Livingstone, Edinburgh, 1987, pp 473495.
2.Macartney, FJ, Zuberbuhler, JR, Anderson, RH. Morphological considerations pertaining to recognition of atrial isomerism. Consequences for sequential chamber localisation. Br Heart J 1980; 44: 657667.
3.Huhta, JC, Smallhorn, JF, Macartney, FJ, Anderson, RH, de Leval, MR. Cross-sectional echocardiographic diagnosis of systemic venous return. Br Heart J 1982; 48: 388403.
4.Sharma, S, Devine, W, Anderson, RH, Zuberbuhler, JR. Identification and analysis of left atrial isomerism. Am J Cardiol 1987; 60: 11571160.
5.Nabarro, D. Two hearts showing peculiarities of the great veins. J Anat Physiol 1903; 37: 382391.
6.Le Pere, RH, Kohler, CM, Klinger, P, Lowry, JK. Intrathoracic venous anomalies. J Thor Cardiovasc Surg 1965; 49: 599614.
7.Edwards, JE. Congenital malformations of the heart and great vessels. I. Malformations of the thoracic veins. In: Gould, SE (ed): Pathology of the Heart and Blood Vessels. Third edition. Charles C Thomas, Springfield, 1968, pp 463478.
8.Dickinson, DF, Wilkinson, JL, Anderson, KR, Smith, A, Ho, SY, Anderson, RH. The cardiac conduction system in situs ambiguus. Circulation 1978; 59: 879887.
9.Ho, SY, Fagg, N, Anderson, RH, Cook, A, Allan, L. Disposition of the atrioventricular conduction tissues in the heart with isomerism of the atrial appendages: its relation to congenital complete heart block. J Am Coll Cardiol 1992; 20: 904910.


Left-sided hepatic vein connected to the coronary sinus

  • László Király (a1), John E. Deanfield (a1) and Marc R. de Leval (a1)


Full text views

Total number of HTML views: 0
Total number of PDF views: 0 *
Loading metrics...

Abstract views

Total abstract views: 0 *
Loading metrics...

* Views captured on Cambridge Core between <date>. This data will be updated every 24 hours.

Usage data cannot currently be displayed