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Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression

  • Ronak Sheth (a1), Roy Varghese (a1) and Kothandam Sivakumar (a1)

Abstract

Left aortic arch with right descending aorta is a rare congenital anomaly. We describe the clinical presentation of this unusual anomaly associated with cardiorespiratory compromise from severe aortic obstruction and left main bronchus compression. The anatomical peculiarities, embryological basis, and surgical solutions are presented.

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Corresponding author

Author for correspondence: Dr K. Sivakumar, MD, DM, Head of Department of Pediatric Cardiology, Institute of Cardiovascular Diseases, Madras Medical Mission, 4A, Dr J J Nagar, Mogappair, Chennai 600089, India. Tel: +91 9444449966; Fax: +91 44 26565859; E-mail: drkumarsiva@hotmail.com

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Cite this article: Sheth R, Varghese R, Sivakumar K. (2018) Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression. Cardiology in the Young 28: 1056–1058. doi: 10.1017/S1047951118000665

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References

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6. Rad, EM, Mortezaeian, H, Pouraliakbar, HR, Hijazi, ZM. Pitfalls of stenting coarctation of an angulated right circumflex aortic arch in Goldenhar syndrome. Ann Pediatr Cardiol 2017; 10: 194196.
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Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression

  • Ronak Sheth (a1), Roy Varghese (a1) and Kothandam Sivakumar (a1)

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