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Imperforate Ebstein's malformation in atrioventricular septal defect

Published online by Cambridge University Press:  19 August 2008

Jeong-Wook Seo ,
Woo Hee Jung  and
Yong Won Park
Jeong-Wook Seo*
Affiliation:
Department of Pathology, Seoul National University College of Medicine and Departments of Pathology and Obstetrics & Gynecology, Yonsei University College of Medicine, Seoul
Woo Hee Jung
Affiliation:
Department of Pathology, Seoul National University College of Medicine and Departments of Pathology and Obstetrics & Gynecology, Yonsei University College of Medicine, Seoul
Yong Won Park
Affiliation:
Department of Pathology, Seoul National University College of Medicine and Departments of Pathology and Obstetrics & Gynecology, Yonsei University College of Medicine, Seoul
*
Department of Pathology, Seoul National University College of Medicine, 28 Yongon-dong Chongno-gu, Seoul 110–460, Korea.
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Summary

Anatomic data are presented of a female abortus with the unusual combination of Ebstein's malformation and atrioventricular septal defect with right isomerism of the atrial appendages, left-hand ventricular topology and discordant ventriculoarterial connection. The common atrioventricular orifice was guarded by an effectively common valve, the right half being guarded by a well-formed three-leaflet valve, but the posterior and left lateral wall of the orifice being deficient of valvar leaflet tissue. The right ventricular inlet was a blind chamber, an imperforate dimple being seen which was surrounded by valvar remnants. The apical trabecular and outlet components of the right ventricle communicated with the left ventricle through an outlet ventricular septal defect in front of the anterosuperior leaflet of the atrioventricular valve, giving the potential clinically for the lesion to be misdiagnosed as double inlet left ventricle.

Type
Brief Reports
Information
Cardiology in the Young , Volume 1 , Issue 2 , April 1991 , pp. 152 - 154
Copyright
Copyright © Cambridge University Press 1991

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References

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