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Hypoplasia of the left heart with discordant ventriculoarterial connections

  • Thomas Borth-Bruhns (a1), Gerhard Ziemer (a2) and Michael Hofbeck (a1)

Abstract

We report the rare combination of a severely hypoplastic left ventricle and discordant ventriculoarterial connections, with associated subpulmonary obstruction of the left ventricular outflow tract. The long tortuous arterial duct originated at an acute angle from the aorta, suggesting that the subpulmonary obstruction developed early in fetal life. Residual flow via the hypoplastic left ventricle to the pulmonary circulation after insertion of an aortopulmonary shunt resulted in haemodynamic deterioration, which was instantly reversed by closing the pulmonary trunk.

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Corresponding author

Correspondence to: Thomas Borth-Bruhns, Herzzentrum Duisburg KWK, Klinik für Kinderkardiologie – Angeborene Herzfehler, Gerrickstrasse 21, D-47137 Duisburg, Germany. Tel: +49 203 451 3660; Fax: +49 203 451 3303; E-mail: tbruhns.chalumeau@t-online.de, Thomas.Borth-Bruhns@EJK.de

References

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References

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Keywords

Hypoplasia of the left heart with discordant ventriculoarterial connections

  • Thomas Borth-Bruhns (a1), Gerhard Ziemer (a2) and Michael Hofbeck (a1)

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