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Hospitalisations of children and adults with Hypoplastic Left Heart Syndrome in Texas from 2009 to 2019

Published online by Cambridge University Press:  12 October 2022

Andrew Well Open the ORCID record for Andrew Well [Opens in a new window] ,
Catherine Dawson Open the ORCID record for Catherine Dawson [Opens in a new window] ,
Gregory Johnson ,
Hanoch Patt ,
Charles D. Fraser ,
Carlos M. Mery  and
Ziv Beckerman
Andrew Well*
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA Department of Surgery and Perioperative Care, University of Texas at Austin Dell Medical School, Austin, TX, USA
Catherine Dawson
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA University of Texas at Austin Dell Medical School, Austin, TX, USA
Gregory Johnson
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA Department of Pediatrics, University of Texas at Austin Dell Medical School, Austin, TX, USA
Hanoch Patt
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA Department of Pediatrics, University of Texas at Austin Dell Medical School, Austin, TX, USA
Charles D. Fraser
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA Department of Surgery and Perioperative Care, University of Texas at Austin Dell Medical School, Austin, TX, USA
Carlos M. Mery
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA Department of Surgery and Perioperative Care, University of Texas at Austin Dell Medical School, Austin, TX, USA
Ziv Beckerman
Affiliation:
Texas Center for Pediatric and Congenital Heart Disease, UT Health Austin and Dell Children’s Medical Center, Austin, TX, USA Department of Surgery and Perioperative Care, University of Texas at Austin Dell Medical School, Austin, TX, USA
*
Author for correspondence: A. Well, MD, MPH, MSHCT, Dell Pediatric Research Institute, 1400 Barbara Jordan BLVD., Office 3.818, Austin, TX 78723, USA. Tel: 512-495-4708; Fax: 512-324-3317. E-mail: andrew.well@austin.utexas.edu
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Abstract

Introduction:

Hypoplastic Left Heart Syndrome accounts for a significant proportion of CHD morbidity and mortality, despite improvements in care and improved survival. This study evaluates number of, reasons for, and trends in discharges of patients with hypoplastic left heart syndrome over 11 years in Texas.

Methods:

The Texas Inpatient Discharge Dataset Public Use File captures almost all discharges in Texas and was reviewed from 2009 to 2019. Discharges of patients ≥5 years of age and diagnosis codes for Hypoplastic Left Heart Syndrome were included. The admitting and principle diagnoses were categorised and all discharges were evaluated for procedures performed. Descriptive and univariate statistical analyses were performed.

Results:

A total of 1024 discharges were identified with a 16.9% annual increase over the study period. Median length of stay was 4 [IQR: 2–8] and there were 17 (1.7%) in-hospital mortalities with no differences across age groups. Seven (17.1%) discharges of patients 25+ years were uninsured, higher than other age groups (p < 0.001). The most common admitting diagnosis was CHD and 224 (21.9%) of discharges included a procedure, including 23 heart transplants. Discharges occurred from 67 different hospitals with 4 (6.0%) representing 71.4% of all discharges.

Conclusions:

Discharges of Hypoplastic Left Heart Syndrome have increased rapidly, particularly in the older age groups and were spread over a large number of hospitals. Further work is needed to understand the interplay between Hypoplastic Left Heart Syndrome and other conditions and care experiences that occur within the general population, which will become more common as this population ages and grows.

Keywords

Hypoplastic Left Heart Syndromeoutcomesresource utilization
Type
Original Article
Information
Cardiology in the Young , Volume 33 , Issue 10 , October 2023 , pp. 1819 - 1827
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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