Skip to main content Accessibility help
×
Home

Echocardiography of hypoplastic left heart syndrome

  • Thieu Nguyen (a1), Michelle Miller (a1), Javier Gonzalez (a2), Katherine Nardell (a1), James Galas (a1), John B. John (a1) (a2), Stan Timofeev (a3), Rich Lambou (a1), Kathryn Douglas (a1) and Gerald Marx (a4)...

Abstract

Echocardiography is critical in the assessment of patients with hypoplastic left heart syndrome. Fundamental techniques and standardised approaches are useful when evaluating patients with hypoplastic left heart syndrome prenatally, after birth, and before the Norwood operation (Stage 1); after the Norwood operation, before and after the superior cavopulmonary anastomosis (Stage 2); before and after the Fontan operation (Stage 3); and for chronic surveillance after the Fontan operation. From foetal assessment to ongoing surveillance after the Fontan procedure, echocardiography remains the primary technique for cardiac monitoring in this growing population of children and adults.

Copyright

Corresponding author

Correspondence to: Dr T. P. Nguyen, MD, All Children's Hospital – Heart Institute of Florida, 2nd Floor Outpatient Care Center, 601 5th Street South, Saint Petersburg, Florida 33701, United States of America. Tel: +1 727 767 3333; Fax: +1 727 767 8990; E-mail: Thieu.nguyen@allkids.org

References

Hide All
1.Tchervenkov, CI, Jacobs, JP, Weinberg, PM, et al. The nomenclature, definition and classification of hypoplastic left heart syndrome. Cardiology in the Young, 2006; 16: 339368.
2.Michelfelder, EC, Gomez, CA, Border, W, Gottliebson, W, Franklin, C. Predictive value of fetal pulmonary venous flow patterns in identifying the need for atrial septoplasty in the newborn with hypoplastic left ventricle. Circulation 2005; 112: 29742979. Epub 31 October 2005.
3.Szwast, A, Tian, Z, McCann, M, Donaghue, D, Rychik, J. Vasoreactive response to maternal hyperoxygenation in the fetus with Hypoplastic Left Heart Syndrome. Circ Cardiovasc Imaging 2010; 3: 172178.
4.Berg, C, Gembruch, O, Gembruch, U, Geipel, A. Doppler indices of the middle cerebral artery in fetuses with cardiac defects theoretically associated with impaired cerebral oxygen delivery in utero: is there a brain-sparing effect? Ultrasound Obstet Gynecol 2009; 34: 666672.
5.Rychik, J, Bush, DM, Spray, TL, et al. Assessment of pulmonary/systemic blood flow ratio after first-stage palliation for hypoplastic left heart syndrome: Development of a new index with the use of Doppler echocardiography. J Thoracic Cardiovasc Surg 2000; 120: 8187.
6.Snider, AR, Serwer, GA, Ritter, SB. Echocardiography in Pediatric Heart Disease. Baltimore, MD: Mosby 1997.
7.Cohen, MS, Marino, BS, McElhinney, DB, et al. Neo-aortic root dilatation and valve regurgitation up to 21 years after staged reconstruction for hypoplastic left heart syndrome. Journal of the American College of Cardiology 2003; 42: 533540.

Keywords

Related content

Powered by UNSILO

Echocardiography of hypoplastic left heart syndrome

  • Thieu Nguyen (a1), Michelle Miller (a1), Javier Gonzalez (a2), Katherine Nardell (a1), James Galas (a1), John B. John (a1) (a2), Stan Timofeev (a3), Rich Lambou (a1), Kathryn Douglas (a1) and Gerald Marx (a4)...

Metrics

Altmetric attention score

Full text views

Total number of HTML views: 0
Total number of PDF views: 0 *
Loading metrics...

Abstract views

Total abstract views: 0 *
Loading metrics...

* Views captured on Cambridge Core between <date>. This data will be updated every 24 hours.

Usage data cannot currently be displayed.