Hostname: page-component-8448b6f56d-dnltx Total loading time: 0 Render date: 2024-04-25T06:04:41.271Z Has data issue: false hasContentIssue false
  • English
  • Français

Early onset of progressive subaortic stenosis after complete repair of tetralogy of Fallot

Published online by Cambridge University Press:  19 August 2008

Victor Grech  and
Anton Mifsud
Victor Grech*
Affiliation:
St. Luke's Hospital, Guardamangia, Malta
Anton Mifsud
Affiliation:
St. Luke's Hospital, Guardamangia, Malta
*
Victor Grech, Paediatric Senior Registrar, St. Luke's Hospital, Guardamangia, Malta. Tel: + 356 241251 Ext: 1471; Fax: +356 240176; E-mail: victor.e.grech@magnet.mt
Get access Rights & Permissions [Opens in a new window]

Abstract

Tetralogy of Fallot is often found in association with a wide variety of other cardiac lesions, but is rarely found in association with lesions causing obstruction to the left ventricular inflow or outflow. Subaortic stenosis has only rarely been reported in association with tetralogy of Fallot. We report a patient with Marfan syndrome who underwent repair of tetralogy of Fallot at five years of age. Discrete and progressive subaortic stenosis developed two years after the surgical correction, in a previously normal and unobstructed left ventricular outflow tract. Surgical removal of the acquired fibrous subaortic shelf was successful. Clinical signs of obstruction within the left ventricular outflow tract after surgical repair of tetralogy of Fallot should prompt further investigation to exclude the onset of acquired subaortic stenosis.

Keywords

Heart defectscongenitaltetralogy of Fallotsubaortic stenosisdiscreteMarfan syndrome
Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 1 , January 2000 , pp. 57 - 59
Copyright
Copyright © Cambridge University Press 2000

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Anderson, RH, Macartney, FJ, Shinebourne, EA, Tynan, M 1987. Fallot's Tetralogy. In: Anderson, RH, Macartney, FJ, Shinebourne, EA, Tynan, M (eds) Paediatric Cardiology. Churchill Livingstone, Edinburgh, p765–798Google Scholar
2.Somerville, J. Congenital heart disease-changes in form and function. Br Heart J 1979; 41: 1–22CrossRefGoogle ScholarPubMed
3.Taylor, NC, Somerville, J. Fixed subaortic stenosis after repair of ostium primum defects. Br Heart J 1981; 45: 689–697CrossRefGoogle ScholarPubMed
4.Glancy, DL, Morrow, AG, Roberts, W. Malformations of the aortic valve in patients with the tetralogy of Fallot. Am Heart J 1968; 76: 755–759CrossRefGoogle ScholarPubMed
5.Jouannon, C, Charrad, R, Durup, F, Bical, O, Favereau, X, Tran Thanh, X, Corcos, T, Souffrant, G, Toussaint, MTetralogy of Fallot and mitral valve stenosis. Arch Mal Coeur Vaiss 1992; 85: 623–626Google ScholarPubMed
6.Pernot, C, Worms, AM, Marcon, F, Admant, P. Williams-Beuren facies with mental retardation and tetralogy of Fallot. Pediatrie 1984; 39: 53–58Google ScholarPubMed
7.Konishi, Y, Tatsuta, N, Miki, S, Chiba, Y, Kao, CTHikasa, Y, Nishioka, K, Ueda, T, Watanabe, T. Combined discrete subaortic stenosis, idiopathic hypertrophic subaortic stenosis and tetralogy of Fallot. Nippon Geka Hokan 1978; 47: 401–410Google ScholarPubMed
8.Silverman, NH, Gerlis, LM, Ho, SY, Anderson, RH. Fibrous obstruction within the left ventricular outflow tract associated with ventricular septal defect: a pathologic study. J Am Coll Cardiol 1995; 25: 475–481CrossRefGoogle ScholarPubMed
9.Sanders, JH, Van Praagh, R, Sade, RM. Tetralogy of Failot with discrete fibrous subaortic stenosis. Chest 1976; 69: 543–544Google Scholar
10.Thomas, L, Foster, E. Membranous subaortic stenosis presenting decades after surgical correction for tetralogy of Fallot. J Am Soc Echocardiogr 1998; 11: 206–208CrossRefGoogle ScholarPubMed