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Cyanosis in a patient after Fontan palliation due to unrecognised hepatic vein to coronary sinus communication

Part of: Atrioventricular Septal Defect (AVSD) Interventional Cardiology Functionally Univentricular Heart Advanced Imaging Cardiac Morphology

Published online by Cambridge University Press:  04 May 2021

Kristin T. Oshiro Open the ORCID record for Kristin T. Oshiro [Opens in a new window] ,
Maria T. Thanjan  and
Ralf J. Holzer
Kristin T. Oshiro
Affiliation:
Division of Pediatric Cardiology, Columbia University Irving Medical Center/NewYork-Presbyterian Morgan Stanley Children’s Hospital, New York, NY, USA
Maria T. Thanjan
Affiliation:
Division of Pediatric Cardiology, Weill Cornell Medicine/NewYork-Presbyterian Komansky Children’s Hospital, New York, NY, USA
Ralf J. Holzer*
Affiliation:
Division of Pediatric Cardiology, Weill Cornell Medicine/NewYork-Presbyterian Komansky Children’s Hospital, New York, NY, USA
*
Author for correspondence: R. J. Holzer, MD, MSc, FACC, FSCAI, David Wallace – Starr Foundation, Professor of Pediatric Cardiology, Chief, Division of Pediatric Cardiology, Director, Pediatric Cardiac Catheterization, NewYork-Presbyterian Komansky Children’s Hospital. Weill Cornell Medicine, Department of Pediatrics, 525 East 68th Street, Room F-677. New York, NY 10065, USA. Tel: 212.746.3561; Fax: 212.746.8373. E-mail: rjh3001@med.cornelledu
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Abstract

A 6-year-old male with heterotaxia, abnormal systemic and pulmonary venous drainage, and a history of Fontan completion presented with desaturations and was found by cardiac catheterisation to have a hepatic vein to coronary sinus connection. This was successfully occluded using an Amplatzer Muscular Ventricular Septal Defect Occluder.

Keywords

Heterotaxiaanomalous hepatic vein connectionFontan
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 11 , November 2021 , pp. 1864 - 1865
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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