Skip to main content Accessibility help

Congenitally palliated scimitar syndrome

  • Massimiliano Cantinotti (a1), Raffaele Giordano (a1) and Isabella Spadoni (a1)


We present a rare case of scimitar syndrome in which the scimitar vessel, collecting all the right pulmonary veins, was stenotic at its junction, with the inferior caval vein and two anomalous vessels, connecting to the same venous collector, draining most of the flow to the left atrium.

We arbitrarily defined this rare anatomical variant as a congenitally palliated scimitar syndrome.


Corresponding author

Correspondence to: R. Giordano, MD, Fondazione G. Monasterio CNR-Regione Toscana, Ospedale del Cuore, via Aurelia Sud, 54100 Massa, Italy. Tel: +39 3297099540; Fax: +39 0585493616; E-mail:


Hide All
1. Rose, C, Vosshenrich, R. Incomplete scimitar syndrome. Cardiol Young 2002; 12: 389390.
2. Legras, A, Guinet, C, Alifano, M, Lepilliez, A, Regnard, JF. A case of variant scimitar syndrome. Chest 2012; 142: 10391041.
3. Neill, CA, Ferencz, C, Sabiston, DC, Sheldon, H. The familial occurrence of hypoplastic right lung with systemic arterial supply and venous drainage “scimitar syndrome”. Bull J Hop Hosp 1960; 107: 115.
4. Konen, E, Raviv-Zilka, L, Cohen, RA, et al. Congenital pulmonary venolobar syndrome: spectrum of helical CT findings with emphasis on computerized reformatting. Radiographics 2003; 23: 11751184.
5. Freedom, RM, Yoo, SJ, Goo, HW, Mikailan, H, Andresom, RH. The bronchopulmonary foregut malformation complex. Cardiol Young 2006; 16: 229251.
6. Takeda, S, Imachi, T, Arimitsu, K, Minami, M, Hayakawa, M. Two cases of scimitar variant. Chest 1994; 105: 292293.
7. Pearl, W. Scimitar variant. Pediatr Cardiol 1987; 8: 139141.
8. Yoo, SJ, Al-Otay, A, Babyn, P. The relationship between scimitar syndrome, so-called scimitar variant, meandering right pulmonary vein, horseshoe lung and pulmonary arterial sling. Cardiol Young 2006; 16: 300304.


Related content

Powered by UNSILO

Congenitally palliated scimitar syndrome

  • Massimiliano Cantinotti (a1), Raffaele Giordano (a1) and Isabella Spadoni (a1)


Full text views

Total number of HTML views: 0
Total number of PDF views: 0 *
Loading metrics...

Abstract views

Total abstract views: 0 *
Loading metrics...

* Views captured on Cambridge Core between <date>. This data will be updated every 24 hours.

Usage data cannot currently be displayed.