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A “congenitally corrected” variant of Ebstein’s anomaly

Published online by Cambridge University Press:  10 January 2018

Rengin Çetin Güvenç
Affiliation:
Department of Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
Gökmen Akgün
Affiliation:
Department of Pediatric Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
Tolga S. Güvenç*
Affiliation:
Department of Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
*
Correspondence to: T. S. Güvenç, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Tıbbiye Street No:13, Kadıköy, Istanbul, Turkey. Tel: +90 216 632 1818; Fax: +90 216 632 7124; E-mail: tsguvenc@gmail.com

Abstract

Ebstein’s anomaly is a rare CHD that is characterised by caudal displacement of the functional tricuspid annulus and a dysfunctional tricuspid valve owing to a failure of proper leaflet coaptation. We present a balanced variant of Ebstein’s anomaly, in which the overgrowth of the septal leaflet had allowed proper coaptation of the tricuspid leaflets, thus preserving the valve function.

Type
Brief Report
Copyright
© Cambridge University Press 2018 

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References

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Güvenç et al. supplementary material 1

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