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Complete atrioventricular block and reversible systolic dysfunction in left ventricular hypertrabeculation/non-compaction with metabolic myopathy

Published online by Cambridge University Press:  08 December 2010

Claudia Stöllberger ,
Josef Finsterer ,
Gottfried H. Sodeck  and
Franz Weidinger
Claudia Stöllberger*
Affiliation:
2nd Medical Department, Krankenanstalt Rudolfstiftung, Juchgasse, Wien, Österreich
Josef Finsterer
Affiliation:
Department of Neurology, Krankenanstalt Rudolfstiftung, Juchgasse, Wien, Österreich
Gottfried H. Sodeck
Affiliation:
2nd Medical Department, Krankenanstalt Rudolfstiftung, Juchgasse, Wien, Österreich
Franz Weidinger
Affiliation:
2nd Medical Department, Krankenanstalt Rudolfstiftung, Juchgasse, Wien, Österreich
*
Correspondence to: Dr C. Stöllberger, 2nd Medical Department, Krankenanstalt Rudolfstiftung, Juchgasse 25, Steingasse 31/18, A-1030 Wien, Österreich. Tel: +43 1 945 42 91; Fax: +43 1 945 42 91; E-mail: claudia.stöllberger@chello.at
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Abstract

A 32-year-old female patient presented with cardiac failure because of systolic dysfunction. Five years before, a DDD pacemaker had been implanted because of complete atrioventricular block. Echocardiographic examination disclosed left ventricular hypertrabeculation/non-compaction. Because of sinus tachycardia, ivabradine was started and the patient’s left ventricular function returned to normal within 4 months. Recurrent creatine-kinase elevation and reduced nicotinamide adenine dinucleotide staining on muscle biopsy suggested metabolic myopathy.

Keywords

Cardiac failurecardiomyopathypacemaker
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 2 , April 2011 , pp. 229 - 232
Copyright
Copyright © Cambridge University Press 2010

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