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Aortic arch advancement for type A interrupted aortic arch with persistent fifth aortic arch type B

  • Ziyad M. Binsalamah (a1), Peter Chen (a1) and Emmett D. McKenzie (a1)


Persistence of the fifth aortic arch is a very rare anomaly, but is clinically relevant when it is associated with coarctation. We report a case of a neonate with type A interrupted aortic arch and severe coarctation of a persistent fifth aortic arch, which was discovered after repair of a left congenital diaphragmatic hernia. The combination of anomalies was discovered intra-operatively following left thoracotomy, and was treated with aortic arch advancement. The postoperative course was uneventful.


Corresponding author

Correspondence to: Z. M. Binsalamah, Michael E. DeBakey Department of Surgery, Division of Congenital Heart Surgery, Baylor College of Medicine, 6621 Fannin St, MC19345H, Houston, TX 77030, United States of America. Tel: +1 832/623-6145; Fax: +1 832/825-1905; E-mail:


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