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Anomalous aortic origin of a coronary artery in siblings with Marfan syndrome*

Published online by Cambridge University Press:  08 December 2010

Julie A. Brothers ,
Matthew A. Harris  and
Stephen M. Paridon
Julie A. Brothers*
Affiliation:
Division of Cardiology, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
Matthew A. Harris
Affiliation:
Division of Cardiology, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
Stephen M. Paridon
Affiliation:
Division of Cardiology, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
*
Correspondence to: J. A. Brothers, M.D., Division of Cardiology, The Children's Hospital of Philadelphia, 34th Street and Civic Center Boulevard, Cardiology, Main Building, 8NW75, Philadelphia, Pennsylvania 19104, United States of America. Tel: 267-426-5700; Fax: 215 590 4978; E-mail: brothersj@email.chop.edu
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Abstract

We report a case of two brothers with Marfan syndrome and coexistent anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva. To our knowledge, this is the first ever report of siblings with Marfan syndrome who also have anomalous aortic origin of a coronary artery. The treatment and management options in the context of sudden death risk are discussed.

Keywords

Coronary artery anomalyconnective tissue disordercongenital cardiac disease
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 2 , April 2011 , pp. 238 - 240
Copyright
Copyright © Cambridge University Press 2010

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Footnotes

*

The submission is with the full knowledge and approval of the above listed co-authors.

References

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