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Ventricular septal defect closure in a patient with achondroplasia

Published online by Cambridge University Press:  20 June 2016

Keisuke Nakanishi*
Affiliation:
Department of Cardiovascular Surgery, School of Medicine, Juntendo University, Tokyo, Japan
Shiori Kawasaki
Affiliation:
Department of Cardiovascular Surgery, School of Medicine, Juntendo University, Tokyo, Japan
Atsushi Amano
Affiliation:
Department of Cardiovascular Surgery, School of Medicine, Juntendo University, Tokyo, Japan
*
Correspondence to: K. Nakanishi, MD, Associate Professor, Department of Cardiovascular Surgery, Juntendo University, 2-1-1, Hongo, Bunkyo-ku, Tokyo 113-8421, Japan. Tel: +81 3 3813 3111; Fax: +81 3 3813 3210; E-mail: knakani@juntendo.ac.jp

Abstract

Achondroplasia with co-morbid CHD is rare, as are reports of surgical treatment for such patients. We present the case of a 13-year-old girl with achondroplasia and ventricular septal defect. Her ventricular septal defect was surgically repaired focussing on the cardiopulmonary bypass flow, healing of the sternum, and her frail neck cartilage. The surgery and recovery were without complications.

Type
Brief Report
Copyright
© Cambridge University Press 2016 

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References

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