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Surgical ablation of a cardiac rhabdomyoma in an infant with tuberous sclerosis

Published online by Cambridge University Press:  19 August 2008

Dagmar Henglein ,
Nabil-Maurice Guirgis  and
Gérard Bloch
Dagmar Henglein*
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
Nabil-Maurice Guirgis
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
Gérard Bloch
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
*
Dr Dagmar Henglein, Hôpital Lariboisière, 6 rue Ambroise Paré, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France. Tel: 33-1-49 95 65 91 (secretary), Tel 31-49 95 84 54 (direct), Fax 33-1-49 95 86 32
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Abstract

Cardiac rhabdomyoma is a rare tumor. Because of its rate of regression, mainly in the first year of life, conservative therapy is generally suggested when diagnosis occurs in infancy. We report surgical ablation of a rhabdomyoma in a 2-month-old boy in whom the tumor extended into the subaortic outflow tract. The tumor, which had a dual attachment to the aortic and mitral valves, was safely removed without any valvar damage. We suggest immediate surgical intervention for those rhabdomyomas which are life-threatening because of their size, location, or arrhythmogenicity.

Keywords

RhabdomyomaCardiac tumor in infancy
Type
Brief Reports
Information
Cardiology in the Young , Volume 8 , Issue 1 , January 1998 , pp. 134 - 135
Copyright
Copyright © Cambridge University Press 1998

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References

1Webb, DW, Thomas, RD, Osborne, JP. Cardiac rhabdomyomas and their association with tuberous sclerosis. Arch Dis Child 1993;68(3): 367–370.CrossRefGoogle ScholarPubMed
2. Arciniegas, E, Hakimi, M, Farooki, ZQ, Truccone, NJ, Green, EW. Primary cardiac tumors in children. J Thorac Cardiovasc Surg 1980;79(4): 582–591.CrossRefGoogle ScholarPubMed
3. Werner, H Jr, Mirlesse, V, Jacquemard, F, Sonigo, P, Delezoide, AL, Gonzales, M, Brunelle, F, Fermont, L, Daffos, F. Prenatal diagnosis of toberous sclerosis. Use of magnetic resonance, imaging and its implications for prognosis. Prenatal Diag 1994; 14(12): 1151–1154.CrossRefGoogle ScholarPubMed
4. Shepherd, CW, Gomez, MR, Lie, JT, Crowson, CS. Causes of death in patients with tuberous sclerosis. Mayo Clinic Proceedings 1991;66(8): 792–796.CrossRefGoogle ScholarPubMed
5. Soria, F, Valdes, M, Garcia, A, Vicente, T, Perez, F, Garcia, J, Cano, A, Roldan, D. The spontaneous regression of a rhabdomyoma of the right ventricle. Rev Espan Cardiol 1991;44(3): 203–206.Google ScholarPubMed
6. Spooner, EW, Farina, MA, Shaher, RM, Foster, ED. Left ventricular rhabdomyoma causing subaortic stenosis - two dimensional echocardiographic appearance. Pediat Cardiol 1982;2: 67–71.CrossRefGoogle ScholarPubMed
7. Nir, A, Tajik, AJ, Freeman, WK, Seward, JB, Offord, KP, Edwards, WD, Mair, DD, Gomez, MR. Tuberous sclerosis and cardiac rhabdomyoma. Amer J Cardiol 1995;76(5): 419–421.CrossRefGoogle ScholarPubMed
8. Muhler, EG, Turniski-Harder, V, Engelhardt, W, von Bernuth, G. Cardiac involvement in tuberous sclerosis. Br Heart J 1994;72(6):584–590.CrossRefGoogle ScholarPubMed
9. Bjorkhem, G, Lundstrom, NR, Lingman, GIntracardiac rhabdomyomas in neonates: report of three cases. Acta Paediat 1992;81(9):712–715.CrossRefGoogle ScholarPubMed
10. Watson, GH. Cardiac rhabdomyomas in tuberous sclerosis. AnnNYAcadSci 1991;615: 50–57.CrossRefGoogle ScholarPubMed