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Pulmonary atresia with intact atrial and ventricular septums, unroofed coronary sinus, and absent aortocoronary arterial connections

Published online by Cambridge University Press:  08 August 2008

Lance K. Erickson
Affiliation:
Department of Pathology, Primary Children’s Medical Center, Salt Lake City, Utah, United States of America
Michael D. Puchalski
Affiliation:
Department of Cardiology, Primary Children’s Medical Center, Salt Lake City, Utah, United States of America
Theodore J. Pysher
Affiliation:
Department of Pathology, Primary Children’s Medical Center, Salt Lake City, Utah, United States of America
Corresponding
E-mail address:

Abstract

A stillborn fetus with pulmonary valvar atresia and intact atrial and ventricular septums also had absence of coronary arterial connections from the aorta and an unroofed coronary sinus. A left superior caval vein drained to the dilated coronary sinus. The left coronary artery was anomalously connected to the proximal branch of the right pulmonary artery, and a fistula from the right ventricle supplied the right coronary artery.

Type
Brief Report
Copyright
Copyright © Cambridge University Press 2008

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References

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