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Anomalous left coronary artery from the right coronary cusp with gene positive apical hypertrophic cardiomyopathy: a case report and literature review

Published online by Cambridge University Press:  17 December 2013

Justin Georgekutty
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Russell R. Cross
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Joanna B. Rosenthal
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Deneen M. Heath
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Pranava Sinha
Affiliation:
Department of Pediatrics, Division of Cardiac Surgery, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
Anitha S. John*
Affiliation:
Department of Pediatrics, Division of Cardiology, Children’s National Medical Center, George Washington University, Washington, District of Columbia, United States of America
*
Correspondence to: Dr A. S. John, MD, PhD, Assistant Professor of Pediatrics and Internal Medicine, Division of Cardiology, Children’s National Medical Center, 111 Michigan Ave NW, West Wing, 3.5, Washington, DC 20010, United States of America. Tel: 202 476 3543; Fax: 202 476 5700; E-mail: anjohn@childrensnational.org

Abstract

In the United States, hypertrophic cardiomyopathy and coronary artery anomalies account for the leading two causes of sudden death in athletes. We present a case of a patient with an anomalous origin of the left main from the right coronary sinus with associated gene-confirmed hypertrophic cardiomyopathy. The patient underwent surgical repair with unroofing of the intramural portion of the left main coronary artery with a good result. We also review the reported cases in the medical literature describing this uncommon association between anomalous coronary artery origin and hypertrophic cardiomyopathy.

Type
Review Articles
Copyright
© Cambridge University Press 2013 

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