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The Abernethy malformation with inferior caval vein hypoplasia: a tailored technique for transcatheter closure and an insight into embryological perspective

  • Ronak Sheth (a1) and Kothandam Sivakumar (a1)

Abstract

Abernethy malformations manifest as hepatopulmonary syndrome, pulmonary vasculopathy, or encephalopathy. A novel intervention in a child with portosystemic shunt and inferior caval vein hypoplasia led to complete normalisation of hypoxia and relief of obstruction in the inferior caval vein. Embryological explanations of venous anomalies may indicate that inferior caval vein anomalies are frequent but under-recognised in patients with Abernethy malformation.

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Corresponding author

Address for correspondence: Dr K. Sivakumar MD, DM, Head of Department of Pediatric Cardiology, Institute of Cardio Vascular Diseases, Madras Medical Mission, 4A, Dr J J Nagar, Mogappair, Chennai 600089, India. Tel: +91 9444449966; Fax +91 44 26565859; E-mail drkumarsiva@hotmail.com

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Cite this article: Sheth R, Sivakumar K. (2018) The Abernethy malformation with inferior caval vein hypoplasia: a tailored technique for transcatheter closure and an insight into embryological perspective. Cardiology in the Young 28: 1169–1171. doi: 10.1017/S1047951118000884

Footnotes

References

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